Pulmonary lesions in tuberous sclerosis: a review of the literature and a case report
Abstract
The article presents a description of a clinical case of a patient with tuberous sclerosis (TS). The identified dermatological manifestations of the disease are comparable to the main diagnostic criteria. The genetically determined phakomatosis, characterized by skin lesions, is a presenting feature, and dermatologists play a leading role in the diagnosis of TS. TS is characterized by a wide range of specific skin manifestations and multiple visceral lesions. The prognosis is determined by the severity and localization of the visceral pathology and does not correlate with the dermatological manifestations. The article provides modern reference data on etiology, clinical features, diagnostic criteria, differential diagnosis, pathomorphology, and treatment.
About the Authors
V. Korovkin
Белорусский государственный медицинский университет
Belarus
Belarus
E. Katebnikova
Белорусский государственный медицинский университет
Belarus
Belarus
V. Belaya
Минский областной противотуберкулезный диспансер
Belarus
Belarus
L. Surkova
Республиканский научно-практический центр пульмонологии и фтизиатрии
Belarus
Belarus
S. Khlopkov
Минский областной противотуберкулезный диспансер
Belarus
Belarus
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Review
For citations:
Korovkin V., Katebnikova E., Belaya V., Surkova L., Khlopkov S. Pulmonary lesions in tuberous sclerosis: a review of the literature and a case report. Healthcare. 2025;1(10):55-62. (In Russ.)
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