Von Willebrand disease in children’s gynecology. Screening, clinical observations
Abstract
The paper describes cases of the clinical course and management of girls with von Willebrand disease. This hemostatic disorder is a variant of the most common hereditary hemorrhagic hemostasiopathies. Therefore, early diagnostic screening for this pathology in both outpatient and inpatient settings is critically important. The analysis of bleeding index using a point-based scale to assess the severity of hemorrhagic syndrome, along with methods for evaluating menstrual blood loss, enables timely detection of von Willebrand disease and other coagulopathies in girls and women in the Republic of Belarus. This approach ensures appropriate medical prevention and treatment, thereby reducing the risk of life-threatening bleeding in these patients. Two clinical cases are presented with detailed descriptions of the clinical, anamnestic, and tactical aspects.
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For citations:
Milosh T. Von Willebrand disease in children’s gynecology. Screening, clinical observations. Healthcare. 2025;(2):4-15. (In Russ.)
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